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An Overview of Inborn Errors of Metabolism manifesting with Primary Adrenal Insufficiency

Primary adrenal insufficiency (PAI) results from an inability to produce adequate amounts of steroid hormones from the adrenal cortex. The most common causes of PAI are autoimmune adrenalitis (Addison disease), infectious diseases, adrenalectomy, neoplasia, medications, and various rare genetic synd...

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Publicado en:Rev Endocr Metab Disord
Autores principales: Hannah-Shmouni, Fady, Stratakis, Constantine A.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2018
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6204320/
https://ncbi.nlm.nih.gov/pubmed/29956047
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s11154-018-9447-2
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