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The physician and hereditary angioedema friend or foe: 62-year diagnostic delay and iatrogenic procedures

BACKGROUND: Hereditary angioedema due to C1 inhibitor deficiency (C1-INH-HAE) is a rare autosomal dominant disease characterized by episodes of acute subcutaneous swelling, and/or recurrent severe abdominal pain. The disease is potentially fatal if the upper-airway is involved. Iatrogenic harm can o...

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Detalhes bibliográficos
Publicado no:Allergy Asthma Clin Immunol
Principais autores: Valerieva, Anna, Cicardi, Marco, Baraniuk, James, Staevska, Maria
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6201585/
https://ncbi.nlm.nih.gov/pubmed/30386388
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13223-018-0275-4
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