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Immune‐Mediated Myocarditis in Fabry Disease Cardiomyopathy
BACKGROUND: Glycosphingolipid accumulation in Fabry cells generates a proinflammatory response that may influence disease evolution and responsiveness to enzyme replacement therapy. This study evaluated incidence, mechanism, and impact of myocarditis in Fabry disease cardiomyopathy (FDCM). METHODS A...
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| Pubblicato in: | J Am Heart Assoc |
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| Autori principali: | , , , , , , , , |
| Natura: | Artigo |
| Lingua: | Inglês |
| Pubblicazione: |
John Wiley and Sons Inc.
2018
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| Soggetti: | |
| Accesso online: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6201436/ https://ncbi.nlm.nih.gov/pubmed/30371172 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/JAHA.118.009052 |
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