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Perspective: A Novel Prognostic for Sickle Cell Disease
Sickle hemoglobin (α(2)β(S)(2)) polymerization drives disease pathophysiology in sickle cell anemia. Fetal hemoglobin (α(2)γ(2)) restricts disease severity by inhibiting the polymerization of sickle hemoglobin in a concentration-dependent manner. Clinical decision-making relies on diagnostic technol...
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| Pubblicato in: | Saudi J Med Med Sci |
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| Autori principali: | , , , |
| Natura: | Artigo |
| Lingua: | Inglês |
| Pubblicazione: |
Medknow Publications & Media Pvt Ltd
2018
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| Soggetti: | |
| Accesso online: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6196691/ https://ncbi.nlm.nih.gov/pubmed/30787839 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/sjmms.sjmms_107_18 |
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