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Molecular basis of cystic fibrosis: from bench to bedside

Cystic fibrosis (CF), is an autosomal recessive disease affecting different organs. The lung disease, characterized by recurrent and chronic bacterial infection and inflammation since infancy, is the main cause of morbidity and precocious mortality of these individuals. The innovative therapies dire...

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Dettagli Bibliografici
Pubblicato in:Ann Transl Med
Autori principali: Dechecchi, Maria Cristina, Tamanini, Anna, Cabrini, Giulio
Natura: Artigo
Lingua:Inglês
Pubblicazione: AME Publishing Company 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6174194/
https://ncbi.nlm.nih.gov/pubmed/30306073
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.21037/atm.2018.06.48
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