A carregar...

Role of Handheld In Vivo Reflectance Confocal Microscopy for the Diagnosis of Fabry Disease: A Case Report

Fabry disease (FD) is a rare X-linked lysosomal storage disorder caused by the deficient activity of the lysosomal enzyme α-galactosidase that leads to a systemic accumulation of globotriaosylceramide. Handheld in vivo reflectance confocal microscopy (HH-RCM) is a useful modern technique in diagnosi...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:Diseases
Main Authors: Cinotti, Elisa, Provvidenziale, Luca, Fimiani, Michele, Perrot, Jean Luc, Cambazard, Frederic, Rubegni, Pietro
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6164009/
https://ncbi.nlm.nih.gov/pubmed/29954050
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/diseases6030055
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!