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Cardiovascular Management of Adults with Marfan Syndrome

Marfan syndrome (MFS) is a disease in which connective tissue becomes weak secondary to fibrillin-1 mutations, resulting in aortic dilatation, aneurysm formation, aortic dissection, aortic regurgitation and mitral valve prolapse. This autosomal dominantly inherited condition, which was first reporte...

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Dades bibliogràfiques
Publicat a:Eur Cardiol
Autors principals: Isekame, Yukiko, Gati, Sabiha, Aragon-Martin, Jose Antonio, Bastiaenen, Rachel, Kondapally Seshasai, Sreenivasa Rao, Child, Anne
Format: Artigo
Idioma:Inglês
Publicat: Radcliffe Cardiology 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6159454/
https://ncbi.nlm.nih.gov/pubmed/30310455
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.15420/ecr/2016:19:2
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