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High hepatic macrophage activation and low liver function in stable Wilson patients - a Danish cross-sectional study

BACKGROUND: Hepatic macrophage (Kupffer cell) hyperplasia is often described in Wilson’s disease (WD). In many liver diseases, Kupffer cell activation is related to disease severity, liver function, and fibrosis but the importance in WD is unknown. Kupffer cell activation can be assessed by the P-co...

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Dettagli Bibliografici
Pubblicato in:Orphanet J Rare Dis
Autori principali: Björklund, Jessica, Laursen, Tea Lund, Sandahl, Thomas Damgaard, Møller, Holger Jon, Vilstrup, Hendrik, Ott, Peter, Grønbæk, Henning
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6150987/
https://ncbi.nlm.nih.gov/pubmed/30241550
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-018-0910-7
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