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Limited effects of long-term enzyme replacement therapy on the cardiac conduction system in Fabry disease

The long-term effects of enzyme replacement therapy (ERT) on cardiac function and the conduction system in Fabry disease are not clearly understood. We report a case of a 48-year-old man with non-classical Fabry disease treated with ERT for 11 years. He was diagnosed with Fabry disease at age 27 yea...

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Dettagli Bibliografici
Pubblicato in:J Cardiol Cases
Autori principali: Kaneda, Tomoya, Takeda, Masahiro, Suematsu, Tetsuro, Yamamoto, Ryusuke, Takata, Mutsuko, Higashikata, Toshinori, Ino, Hidekazu, Tsujibata, Akihiko, Hayashi, Kenshi, Fujino, Noboru, Kawashiri, Masa-aki
Natura: Artigo
Lingua:Inglês
Pubblicazione: Japanese College of Cardiology 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6149592/
https://ncbi.nlm.nih.gov/pubmed/30279886
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jccase.2018.01.004
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