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Progressive familial intrahepatic cholestasis: diagnosis, management, and treatment

Progressive familial intrahepatic cholestasis (PFIC) is a group of autosomal recessive cholestatic liver diseases which are subgrouped according to the genetic defect, clinical presentation, laboratory findings and liver histology. Progressive liver fibrosis, cirrhosis, and end stage liver disease (...

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Publicado en:Hepat Med
Autores principales: Gunaydin, Mithat, Bozkurter Cil, Asudan Tugce
Formato: Artigo
Lenguaje:Inglês
Publicado: Dove Medical Press 2018
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6136920/
https://ncbi.nlm.nih.gov/pubmed/30237746
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2147/HMER.S137209
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