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Hemophagocytic lymphohistiocytosis and congenital factor VII deficiency: a case report
BACKGROUND: Hemophagocytic lymfohistiocytosis (HLH) is a rare, life-threatening hyperinflammation, characterized by immune system over-activation resulting in hemophagocytosis. HLH could appear as a primary disease caused by mutations of immune-regulatory genes, or develop as a result of viral or ba...
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| Yayımlandı: | BMC Med Genet |
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| Asıl Yazarlar: | , , , , |
| Materyal Türü: | Artigo |
| Dil: | Inglês |
| Baskı/Yayın Bilgisi: |
BioMed Central
2018
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| Konular: | |
| Online Erişim: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6134588/ https://ncbi.nlm.nih.gov/pubmed/30208845 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12881-018-0673-y |
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