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A case of bulbospinal muscular atrophy with large fasciculation manifesting as spinal myoclonus

OBJECTIVE: This paper reports a patient with bulbospinal muscular atrophy (BSMA) who presented with spinal myoclonus, documented by video and surface electromyography. CASE REPORT: A 66-year-old man had progressive gait disturbance, dysphagia, and easy fatigability of all extremities over a period o...

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Vydáno v:Clin Neurophysiol Pract
Hlavní autoři: Inoue, Manabu, Kojima, Yasuhiro, Kanda, Masutaro, Tsuzaki, Koji, Shibata, Yoko, Hamano, Toshiaki, Shibasaki, Hiroshi
Médium: Artigo
Jazyk:Inglês
Vydáno: Elsevier 2017
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6123898/
https://ncbi.nlm.nih.gov/pubmed/30214972
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.cnp.2017.01.001
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