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Acute respiratory failure as presentation of late-onset Pompe disease complicating the diagnostic process as a labyrinth: a case report

BACKGROUND: Acute respiratory failure can be triggered by several causes, either of pulmonary or extra-pulmonary origin. Pompe disease, or type II glycogen storage disease, is a serious and often fatal disorder, due to a pathological accumulation of glycogen caused by a defective activiy of acid α-g...

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Pubblicato in:Multidiscip Respir Med
Autori principali: Menzella, Francesco, Codeluppi, Luca, Lusuardi, Mirco, Galeone, Carla, Valzania, Franco, Facciolongo, Nicola
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6119261/
https://ncbi.nlm.nih.gov/pubmed/30186604
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s40248-018-0145-4
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