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Hereditary hemorrhagic telangiectasia: diagnosis and management from the hematologist’s perspective

Hereditary hemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu syndrome, is an autosomal dominant disorder that causes abnormal blood vessel formation. The diagnosis of hereditary hemorrhagic telangiectasia is clinical, based on the Curaçao criteria. Genetic mutations that have been id...

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Publicado en:Haematologica
Autores principales: Kritharis, Athena, Al-Samkari, Hanny, Kuter, David J
Formato: Artigo
Lenguaje:Inglês
Publicado: Ferrata Storti Foundation 2018
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6119150/
https://ncbi.nlm.nih.gov/pubmed/29794143
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3324/haematol.2018.193003
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