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A female infant with phacomatosis pigmentovascularis and congenital chylous ascites: A case report
RATIONALE: Phacomatosis pigmentovascularis (PPV) is a rare syndrome characterized by capillary malformation and pigmentary nevus. Congenital chylous ascites (CCA) is also a rare disease that results from maldevelopment of the lymphatic system. We report a case of a 5-month-old girl, who had both PPV...
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| Publicat a: | Medicine (Baltimore) |
|---|---|
| Autors principals: | , , , , |
| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
Wolters Kluwer Health
2018
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6112933/ https://ncbi.nlm.nih.gov/pubmed/30142845 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MD.0000000000012012 |
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