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Gorlin-Goltz Syndrome: A Rare Case Report

Gorlin-Goltz syndrome (GGS) is an autosomal dominant disorder with a high degree of penetrance and variable expressivity. It is a rare phakomatosis characterized by multiple odontogenic keratocysts (OKCs), bifid ribs, and other abnormalities. The incidence of the GGS is estimated at 1 in 57,000–1 in...

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Publicado en:Contemp Clin Dent
Autores principales: Kumar, Naveen N., Padmashree, S., Jyotsna, T. R., Shastry, Shilpa Padar
Formato: Artigo
Lenguaje:Inglês
Publicado: Medknow Publications & Media Pvt Ltd 2018
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6104368/
https://ncbi.nlm.nih.gov/pubmed/30166848
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/ccd.ccd_96_18
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