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Subclinical Left Ventricular Dysfunction is Influenced by Genotype Severity in Patients with Cystic Fibrosis

BACKGROUND AND OBJECTIVE: Over 2000 genotypes in the cystic fibrosis (CF) gene have been described. These genotypic differences result in variable clinical manifestations of CF, with severity of disease dependent on CF transmembrane conductance (CFTR) protein function. CFTR is widely distributed in...

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Detalhes bibliográficos
Publicado no:Clin Med Insights Circ Respir Pulm Med
Main Authors: Pallin, Michael, Keating, Dominic, Kaye, David M, Kotsimbos, Tom, Wilson, John W
Formato: Artigo
Idioma:Inglês
Publicado em: SAGE Publications 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6102756/
https://ncbi.nlm.nih.gov/pubmed/30147387
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1179548418794154
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