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Hemophagocytic Lymphohistiocytosis Complicating Systemic Sarcoidosis
Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hyperinflammatory syndrome characterized by histiocyte proliferation and hemophagocytosis. Primary HLH is caused by genetic defects, whereas secondary HLH occurs in the setting of underlying diseases, such as infections, malignanci...
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| Publicat a: | Cureus |
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| Autors principals: | , , |
| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
Cureus
2018
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6101461/ https://ncbi.nlm.nih.gov/pubmed/30131931 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.7759/cureus.2838 |
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