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Atypical Distribution of Late Gadolinium Enhancement of the Left Ventricle on Cardiac Magnetic Resonance in Classical Anderson-Fabry Disease

Anderson-Fabry disease (AFD) is an X-linked lysosomal storage disorder caused by a deficiency of alpha-galactosidase A. Approximately 50% of patients with AFD may have cardiac involvement. Gadolinium-enhanced cardiac magnetic resonance (CMR) is useful for the diagnosis of cardiac involvement of AFD...

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Detalhes bibliográficos
Publicado no:J Belg Soc Radiol
Main Authors: Kasuya, Shusuke, Suzuki, Masayo, Inaoka, Tsutomu, Odashima, Masayuki, Nakatsuka, Tomoya, Ishikawa, Rumiko, Tokuyama, Wataru, Terada, Hitoshi
Formato: Artigo
Idioma:Inglês
Publicado em: Ubiquity Press 2016
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6100657/
https://ncbi.nlm.nih.gov/pubmed/30151436
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.5334/jbr-btr.906
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