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Congenital aniridia: etiology, manifestations and management

Congenital aniridia manifests as total or partial absence of the iris caused most commonly by mutations in PAX6, FOXC1, PITX2, and CYP1B1. Recently two new genes, FOXD3 and TRIM44, have also been implicated in isolated studies. We discuss the genotype-phenotype correlations for the main implicated g...

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Publicat a:Expert Rev Ophthalmol
Autors principals: Samant, Monica, Chauhan, Bharesh K., Lathrop, Kira L., Nischal, Ken K.
Format: Artigo
Idioma:Inglês
Publicat: 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6086384/
https://ncbi.nlm.nih.gov/pubmed/30100922
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1586/17469899.2016.1152182
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