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Riociguat use in sickle cell related chronic thromboembolic pulmonary hypertension: A case series

Adults with sickle cell disease can develop pulmonary hypertension from a multitude of etiologies. Classified as WHO Group 5, there are no therapies approved for the treatment of sickle cell disease-pulmonary hypertension. Thromboembolic disease is prevalent in sickle cell disease and can lead to pu...

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Detalhes bibliográficos
Publicado no:Pulm Circ
Main Authors: Weir, Nargues A., Conrey, Anna, Lewis, Denise, Mehari, Alem
Formato: Artigo
Idioma:Inglês
Publicado em: SAGE Publications 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6083805/
https://ncbi.nlm.nih.gov/pubmed/30033820
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/2045894018791802
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