Cargando...

Prenylated retinal ciliopathy protein RPGR interacts with PDE6δ and regulates ciliary localization of Joubert syndrome-associated protein INPP5E

Ciliary trafficking defects underlie the pathogenesis of severe human ciliopathies, including Joubert Syndrome (JBTS), Bardet-Biedl Syndrome, and some forms of retinitis pigmentosa (RP). Mutations in the ciliary protein RPGR (retinitis pigmentosa GTPase regulator) are common causes of RP-associated...

Descrición completa

Gardado en:
Detalles Bibliográficos
Publicado en:Hum Mol Genet
Main Authors: Rao, Kollu N., Zhang, Wei, Li, Linjing, Anand, Manisha, Khanna, Hemant
Formato: Artigo
Idioma:Inglês
Publicado: Oxford University Press 2016
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6078598/
https://ncbi.nlm.nih.gov/pubmed/28172980
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddw281
Tags: Engadir etiqueta
Sen Etiquetas, Sexa o primeiro en etiquetar este rexistro!