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Secreted Phospholipases A(2) in Hereditary Angioedema With C1-Inhibitor Deficiency

BACKGROUND: Hereditary angioedema (HAE) caused by deficiency (type I) or dysfunction (type II) of the C1 inhibitor protein (C1-INH-HAE) is a disabling, potentially fatal condition characterized by recurrent episodes of swelling. We have recently found that patients with C1-INH-HAE have increased pla...

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Detalhes bibliográficos
Publicado no:Front Immunol
Main Authors: Loffredo, Stefania, Ferrara, Anne Lise, Bova, Maria, Borriello, Francesco, Suffritti, Chiara, Veszeli, Nóra, Petraroli, Angelica, Galdiero, Maria Rosaria, Varricchi, Gilda, Granata, Francescopaolo, Zanichelli, Andrea, Farkas, Henriette, Cicardi, Marco, Lambeau, Gérard, Marone, Gianni
Formato: Artigo
Idioma:Inglês
Publicado em: Frontiers Media S.A. 2018
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6064723/
https://ncbi.nlm.nih.gov/pubmed/30083168
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2018.01721
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