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Mitochondrial DNA transcription and translation: clinical syndromes

Diagnosing primary mitochondrial diseases is challenging in clinical practice. Although, defective oxidative phosphorylation (OXPHOS) is the common final pathway, it is unknown why different mtDNA or nuclear mutations result in largely heterogeneous and often tissue -specific clinical presentations....

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Shranjeno v:
Bibliografske podrobnosti
izdano v:Essays Biochem
Main Authors: Boczonadi, Veronika, Ricci, Giulia, Horvath, Rita
Format: Artigo
Jezik:Inglês
Izdano: Portland Press Ltd. 2018
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC6056718/
https://ncbi.nlm.nih.gov/pubmed/29980628
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1042/EBC20170103
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