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Association and diagnostic utility of diastolic dysfunction and myocardial fibrosis in patients with Fabry disease

OBJECTIVES: Current guidelines highlight important therapy implications of cardiac fibrosis in patients with Fabry disease (FD). However, association between morphological and functional impairments with cardiac fibrosis in hereditary cardiomyopathies remains elusive. We investigated the association...

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Detalhes bibliográficos
Publicado no:Open Heart
Main Authors: Liu, Dan, Oder, Daniel, Salinger, Tim, Hu, Kai, Müntze, Jonas, Weidemann, Frank, Herrmann, Sebastian, Ertl, Georg, Wanner, Christoph, Frantz, Stefan, Störk, Stefan, Nordbeck, Peter
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Publishing Group 2018
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6045729/
https://ncbi.nlm.nih.gov/pubmed/30018776
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/openhrt-2018-000803
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