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Altered Gene Expression in Prefrontal Cortex of a Fabry Disease Mouse Model

Fabry disease is an X-chromosome linked hereditary disease that is caused by loss of function mutations in the α-galactosidase A (α-Gal A) gene, resulting in defective glycolipid degradation and subsequent accumulation of globotriaosylceramide (Gb3) in different tissues, including vascular endotheli...

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Detalhes bibliográficos
Publicado no:Front Mol Neurosci
Main Authors: Kummer, Kai K., Kalpachidou, Theodora, Mitrić, Miodrag, Langeslag, Michiel, Kress, Michaela
Formato: Artigo
Idioma:Inglês
Publicado em: Frontiers Media S.A. 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6036252/
https://ncbi.nlm.nih.gov/pubmed/30013462
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnmol.2018.00201
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