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Carbohydrate status in patients with phenylketonuria

BACKGROUND: In patients with phenylketonuria (PKU), a low-phenylalanine (Phe) diet supplemented with low-protein foods and a Phe-free amino acid mixture favors a dietary intake rich in carbohydrates, but little is known about how these molecules are metabolized in this setting. The objective of the...

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Dettagli Bibliografici
Pubblicato in:Orphanet J Rare Dis
Autori principali: Couce, María L., Sánchez-Pintos, Paula, Vitoria, Isidro, De Castro, María-José, Aldámiz-Echevarría, Luís, Correcher, Patricia, Fernández-Marmiesse, Ana, Roca, Iria, Hermida, Alvaro, Martínez-Olmos, Miguel, Leis, Rosaura
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6020344/
https://ncbi.nlm.nih.gov/pubmed/29945661
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-018-0847-x
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