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A case of Metaplastic atrophic gastritis in immune Dysregulation, Polyendocrinopathy, Enteropathy, X-linked (IPEX) syndrome

BACKGROUND: Autoimmune metaplastic atrophic gastritis is a chronic progressive inflammatory condition. The clinical spectrum includes pernicious anemia, atrophic gastritis, antibodies to parietal cell antigens and intrinsic factor, achlorhydria, hypergastrinemia and carcinoma. It is rare in paediatr...

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Publicado en:BMC Pediatr
Autores principales: Luo, Youyou, Chen, Jie, Fang, Youhong, Lou, Jingan, Yu, Jindan
Formato: Artigo
Lenguaje:Inglês
Publicado: BioMed Central 2018
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6002972/
https://ncbi.nlm.nih.gov/pubmed/29907148
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12887-018-1169-9
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