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A Case Report of Pulmonary Exacerbation after Initiation of Lumacaftor/Ivacaftor Therapy in a CF Female with Complicated Lung Disease

Novel targeted treatments for Cystic Fibrosis give rise to new hope for an ever-growing number of CF patients with various mutations. However, very little evidence and guidelines exist to steer clinical decisions regarding patients whose illness takes an unexpected course. In such cases, the benefit...

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Publicat a:Case Rep Pulmonol
Autors principals: Hatziagorou, Elpis, Kouroukli, Eleana, Georgopoulou, Vasiliki, Tsanakas, John
Format: Artigo
Idioma:Inglês
Publicat: Hindawi 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5998152/
https://ncbi.nlm.nih.gov/pubmed/30002941
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2018/8394370
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