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Food as a trigger for abdominal angioedema attacks in patients with hereditary angioedema

BACKGROUND: Hereditary angioedema with C1 inhibitor deficiency (C1-INH-HAE) is a rare inherited disease. In most HAE-affected subjects, defined trigger factors precede angioedema attacks. Mechanisms of how trigger factors stimulate the contact activation pathway with bradykinin generation are not we...

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Detalhes bibliográficos
Publicado no:Orphanet J Rare Dis
Main Authors: Steiner, Urs C., Kölliker, Lea, Weber-Chrysochoou, Christina, Schmid-Grendelmeier, Peter, Probst, Elsbeth, Wuillemin, Walter A., Helbling, Arthur
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2018
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5987415/
https://ncbi.nlm.nih.gov/pubmed/29866145
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-018-0832-4
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