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Abnormalities in Skeletal Muscle Myogenesis, Growth, and Regeneration in Myotonic Dystrophy

Myotonic dystrophy type 1 (DM1) and 2 (DM2) are autosomal dominant degenerative neuromuscular disorders characterized by progressive skeletal muscle weakness, atrophy, and myotonia with progeroid features. Although both DM1 and DM2 are characterized by skeletal muscle dysfunction and also share othe...

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Dades bibliogràfiques
Publicat a:Front Neurol
Autors principals: André, Laurène M., Ausems, C. Rosanne M., Wansink, Derick G., Wieringa, Bé
Format: Artigo
Idioma:Inglês
Publicat: Frontiers Media S.A. 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5985300/
https://ncbi.nlm.nih.gov/pubmed/29892259
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fneur.2018.00368
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