A carregar...

Retinal and optic nerve degeneration in α-mannosidosis

BACKGROUND: α-mannosidosis is a rare, autosomal-recessive, lysosomal storage disease caused by a deficient activity of α-mannosidase. Typical symptoms include intellectual, motor and hearing impairment, facial coarsening, and musculoskeletal abnormalities. Ocular pathologies reported previously were...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:Orphanet J Rare Dis
Main Authors: Matlach, Juliane, Zindel, Thea, Amraoui, Yasmina, Arash-Kaps, Laila, Hennermann, Julia B., Pitz, Susanne
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5984778/
https://ncbi.nlm.nih.gov/pubmed/29859105
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-018-0829-z
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!