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Oxidative stress-driven pulmonary inflammation and fibrosis in a mouse model of human ataxia-telangiectasia

Lung failure is responsible for significant morbidity and is a frequent cause of death in ataxia-telangiectasia (A-T). Disturbance in the redox balance of alveolar epithelial cells must be considered as a causal factor for respiratory disease in A-T. To investigate bronchoalveolar sensitivity to rea...

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Detalhes bibliográficos
Publicado no:Redox Biol
Main Authors: Duecker, Ruth, Baer, Patrick, Eickmeier, Olaf, Strecker, Maja, Kurz, Jennifer, Schaible, Alexander, Henrich, Dirk, Zielen, Stefan, Schubert, Ralf
Formato: Artigo
Idioma:Inglês
Publicado em: Elsevier 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5975220/
https://ncbi.nlm.nih.gov/pubmed/29172151
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.redox.2017.11.006
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