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Invertebrate models of lamin diseases

Lamins are evolutionarily conserved nuclear intermediate filament proteins. They provide structural support for the nucleus and help regulate many other nuclear activities. Mutations in human lamin genes, and especially in the LMNA gene, cause numerous diseases, termed laminopathies, including muscl...

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Dades bibliogràfiques
Publicat a:Nucleus
Autors principals: Rzepecki, Ryszard, Gruenbaum, Yosef
Format: Artigo
Idioma:Inglês
Publicat: Taylor & Francis 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5973256/
https://ncbi.nlm.nih.gov/pubmed/29557730
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/19491034.2018.1454166
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