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Longitudinal Changes in White Matter Fractional Anisotropy in Adult-Onset Niemann-Pick Disease Type C Patients Treated with Miglustat

Niemann-Pick disease type C (NPC) is a rare neurometabolic disorder resulting in impaired intracellular lipid trafficking. The only disease-modifying treatment currently available is miglustat, an iminosugar that inhibits the accumulation of lipid metabolites in neurons and other cells. This longitu...

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Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:JIMD Rep
Egile Nagusiak: Bowman, Elizabeth A., Velakoulis, Dennis, Desmond, Patricia, Walterfang, Mark
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Springer Berlin Heidelberg 2017
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC5953894/
https://ncbi.nlm.nih.gov/pubmed/28710748
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2017_42
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