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Immune-mediated pathology in Duchenne muscular dystrophy

Immunological and inflammatory processes downstream of dystrophin deficiency as well as metabolic abnormalities, defective autophagy, and loss of regenerative capacity all contribute to muscle pathology in Duchenne muscular dystrophy (DMD). These downstream cascades offer potential avenues for pharm...

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Detalhes bibliográficos
Publicado no:Sci Transl Med
Main Authors: Rosenberg, Amy S., Puig, Montserrat, Nagaraju, Kanneboyina, Hoffman, Eric P., Villalta, S. Armando, Rao, V. Ashutosh, Wakefield, Lalage M., Woodcock, Janet
Formato: Artigo
Idioma:Inglês
Publicado em: 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5951380/
https://ncbi.nlm.nih.gov/pubmed/26246170
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1126/scitranslmed.aaa7322
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