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Immune-mediated pathology in Duchenne muscular dystrophy

Immunological and inflammatory processes downstream of dystrophin deficiency as well as metabolic abnormalities, defective autophagy, and loss of regenerative capacity all contribute to muscle pathology in Duchenne muscular dystrophy (DMD). These downstream cascades offer potential avenues for pharm...

Täydet tiedot

Tallennettuna:
Bibliografiset tiedot
Julkaisussa:Sci Transl Med
Päätekijät: Rosenberg, Amy S., Puig, Montserrat, Nagaraju, Kanneboyina, Hoffman, Eric P., Villalta, S. Armando, Rao, V. Ashutosh, Wakefield, Lalage M., Woodcock, Janet
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: 2015
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC5951380/
https://ncbi.nlm.nih.gov/pubmed/26246170
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1126/scitranslmed.aaa7322
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