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Chagasic cardiomyopathy and Pompe disease: case report

Background: Pompe disease is a lysosomal storage disease with an autosomal recessive inheritance characterized by an insufficient activity of the acid alpha-glucosidase enzyme. The incidence varies from 1:40000 to 1:200000 live births and cardiac involvement in adults is rare. Chagas disease is an i...

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Publicat a:Am J Cardiovasc Dis
Autors principals: de Morais, Rafael OB, Chaves-Markman, Ândrea V, Miranda, Anna PP, Amorim, Ingrid G, Cavalcanti, Maria da GA de M, Markman, Manuel, Markman-Filho, Brivaldo
Format: Artigo
Idioma:Inglês
Publicat: e-Century Publishing Corporation 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5944812/
https://ncbi.nlm.nih.gov/pubmed/29755837
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