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Alpha-1-antitrypsin deficiency: increasing awareness and improving diagnosis
Alpha-1-antitrypsin deficiency (AATD) is a hereditary disorder that is characterized by a low serum level of alpha-1-antitrypsin (AAT). The loss of anti-inflammatory and antiproteolytic functions, together with pro-inflammatory effects of polymerized AAT contribute to protein degradation and increas...
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| Publicat a: | Ther Adv Respir Dis |
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| Autors principals: | , |
| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
SAGE Publications
2015
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC5933657/ https://ncbi.nlm.nih.gov/pubmed/26341117 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1753465815602162 |
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