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Atypical Osteosarcomas in Werner Syndrome (Adult Progeria)

Werner syndrome (WS), adult progeria, is more common in Japan than elsewhere. It predisposes to osteosarcoma (OS) and five other rare tumors. To determine if and how OS is atypical in this genetic disorder, we studied the characteristics of ten Japanese cases with respect to clinical features, patho...

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Publicado en:Jpn J Cancer Res
Autores principales: Ishikawa, Yuichi, Miller, Robert W., Machinami, Rikuo, Sugano, Haruo, Goto, Makoto
Formato: Artigo
Lenguaje:Inglês
Publicado: Blackwell Publishing Ltd 2000
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5926298/
https://ncbi.nlm.nih.gov/pubmed/11123436
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/j.1349-7006.2000.tb00924.x
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