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Undiagnosed Partial Ornithine Transcarbamylase Deficiency Presenting Postoperatively as Agitated Delirium

Partial ornithine transcarbamylase deficiency (pOTCD), an enzymatic defect within the urea cycle, is an increasingly recognized etiology for hyperammonemia of unclear source following a stressor within female adults. Here we present a case of newly diagnosed pOTCD following a systemic stressor and p...

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Publicat a:Neurohospitalist
Autors principals: Goldstein, E. D., Cannistraro, R., Atwal, P. S., Meschia, J. F.
Format: Artigo
Idioma:Inglês
Publicat: SAGE Publications 2017
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5882010/
https://ncbi.nlm.nih.gov/pubmed/29623158
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1941874417729983
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