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Glutaric Acidemia Type 1: A Case of Infantile Stroke

Background: Glutaric acidemia Type 1 (GA-1) is an autosomal recessively inherited metabolic disorder which is associated with GCDH gene mutations which alters the glutaryl-CoA dehydrogenase, an enzyme playing role in the catabolic pathways of the amino acids lysine, hydroxylysine, and tryptophan. Cl...

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Dettagli Bibliografici
Pubblicato in:JIMD Rep
Autori principali: Kaya Ozcora, Gül Demet, Gokay, Songul, Canpolat, Mehmet, Kardaş, Fatih, Kendirci, Mustafa, Kumandaş, Sefer
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer Berlin Heidelberg 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5874218/
https://ncbi.nlm.nih.gov/pubmed/28411331
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2017_26
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