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Clinicopathologic and Molecular Characteristics of Familial Cherubism with Associated Odontogenic Tumorous Proliferations

Cherubism is a rare autosomal dominant condition affecting the jaws and caused by mutations in the gene encoding for the adapter protein SH3BP2 that maps to chromosome 4p16.3. Cherubism is characterized by symmetrically developing bone lesions in the maxilla and mandible. The lesions have been radio...

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Publicado en:Head Neck Pathol
Autores principales: Argyris, Prokopios P., Gopalakrishnan, Rajaram, Hu, Ying, Reichenberger, Ernst J., Koutlas, Ioannis G.
Formato: Artigo
Lenguaje:Inglês
Publicado: Springer US 2017
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5873491/
https://ncbi.nlm.nih.gov/pubmed/28721660
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s12105-017-0837-7
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