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Coagulopathy in Zellweger spectrum disorders: a role for vitamin K

INTRODUCTION: Zellweger spectrum disorders (ZSDs) are caused by an impairment of peroxisome biogenesis, resulting in multiple metabolic abnormalities. This leads to a range of symptoms, including hepatic dysfunction and coagulopathy. This study evaluated the incidence and severity of coagulopathy an...

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Dettagli Bibliografici
Pubblicato in:J Inherit Metab Dis
Autori principali: Zeynelabidin, Sara, Klouwer, Femke C. C., Meijers, Joost C. M., Suijker, Monique H., Engelen, Marc, Poll-The, Bwee Tien, van Ommen, C. Heleen
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer Netherlands 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5830475/
https://ncbi.nlm.nih.gov/pubmed/29139025
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10545-017-0113-8
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