Cargando...

ENG mutational mosaicism in a family with hereditary hemorrhagic telangiectasia

BACKGROUND: Hereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant genetic disorder caused by mutations in ENG,ACVRL1, or SMAD4. Around 90% of HHT patients present with a heterozygous pathogenic genetic variation. Almost all cases of HHT have a family history. Very few cases are de nov...

Descripción completa

Guardado en:
Detalles Bibliográficos
Publicado en:Mol Genet Genomic Med
Autores principales: Tørring, Pernille M., Kjeldsen, Anette D., Ousager, Lilian Bomme, Brusgaard, Klaus
Formato: Artigo
Lenguaje:Inglês
Publicado: John Wiley and Sons Inc. 2017
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5823686/
https://ncbi.nlm.nih.gov/pubmed/29243366
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/mgg3.361
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!