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Niemann-Pick disease type B: HRCT assessment of pulmonary involvement

OBJECTIVE: To analyze HRCT findings in patients with Niemann-Pick disease (NPD) type B, in order to determine the frequency of HRCT patterns and their distribution in the lung parenchyma, as well as the most common clinical characteristics. METHODS: We studied 13 patients (3 males and 10 females) ag...

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Detalles Bibliográficos
Publicado en:J Bras Pneumol
Autores principales: Freitas, Heloisa Maria Pereira, Mançano, Alexandre Dias, Rodrigues, Rosana Souza, Hochhegger, Bruno, Torres, Pedro Paulo Teixeira e Silva, Escuissato, Dante, Araujo, Cesar Augusto, Marchiori, Edson
Formato: Artigo
Lenguaje:Inglês
Publicado: Sociedade Brasileira de Pneumologia e Tisiologia 2017
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC5792045/
https://ncbi.nlm.nih.gov/pubmed/29340494
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/S1806-37562017000000062
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