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Niemann-Pick disease type B: HRCT assessment of pulmonary involvement
OBJECTIVE: To analyze HRCT findings in patients with Niemann-Pick disease (NPD) type B, in order to determine the frequency of HRCT patterns and their distribution in the lung parenchyma, as well as the most common clinical characteristics. METHODS: We studied 13 patients (3 males and 10 females) ag...
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| Publicado en: | J Bras Pneumol |
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| Autores principales: | , , , , , , , |
| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
Sociedade Brasileira de Pneumologia e Tisiologia
2017
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC5792045/ https://ncbi.nlm.nih.gov/pubmed/29340494 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/S1806-37562017000000062 |
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