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Pleuroparenchymal fibroelastosis: report of two cases in Brazil

Pleuroparenchymal fibroelastosis (PPFE) is a rare lung disease. It can be idiopathic or associated with any one of various conditions. To our knowledge, this is the first report of two cases of PPFE in Brazil. Our first patient presented with pleural and subpleural fibrosis in the upper lobes; a spi...

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Dettagli Bibliografici
Pubblicato in:J Bras Pneumol
Autori principali: Gomes, Paula Silva, Shiang, Christina, Szarf, Gilberto, Coletta, Ester Nei Aparecida Martins, Pereira, Carlos Alberto de Castro
Natura: Artigo
Lingua:Inglês
Pubblicazione: Sociedade Brasileira de Pneumologia e Tisiologia 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5790665/
https://ncbi.nlm.nih.gov/pubmed/28125151
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/S1806-37562016000000045
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