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Disease-associated protein seeding suggests a dissociation between misfolded protein accumulation and neurodegeneration in prion disease

Chronic neurodegenerative diseases, such as prion diseases or Alzheimer's disease, are associated with progressive accumulation of host proteins which misfold and aggregate. Neurodegeneration is restricted to specific neuronal populations which show clear accumulation of misfolded proteins, whi...

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Detalhes bibliográficos
Publicado no:Prion
Main Authors: Alibhai, James, Diack, Abigail, Manson, Jean
Formato: Artigo
Idioma:Inglês
Publicado em: Taylor & Francis 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC5786362/
https://ncbi.nlm.nih.gov/pubmed/29023184
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/19336896.2017.1378289
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