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A Mutation in INSR in a Child Presenting with Severe Acanthosis Nigricans

Rabson-Mendenhall syndrome (RMS) is an autosomal recessive disorder due to mutations in the insulin receptor gene (INSR) which is mapped to 19p13.2. RMS is characterized by acanthosis nigricans, generalized lanugo, tooth and nail dysplasia, high nasal bridge, and growth retardation. A 5-year-old fem...

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Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:J Clin Res Pediatr Endocrinol
Egile Nagusiak: Tuhan, Hale, Ceylaner, Serdar, Nalbantoğlu, Özlem, Acar, Sezer, Abacı, Ayhan, Böber, Ece, Demir, Korcan
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Galenos Publishing 2017
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC5785646/
https://ncbi.nlm.nih.gov/pubmed/28663160
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4274/jcrpe.4577
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