Assessment of p.Phe508del-CFTR functional restoration in pediatric primary cystic fibrosis airway epithelial cells

BACKGROUND: Mutations in the cystic fibrosis transmembrane regulator (CFTR) gene can reduce function of the CFTR ion channel activity and impair cellular chloride secretion. The gold standard method to assess CFTR function of ion transport using the Ussing chamber requires a high number of airway ep...

Täydet tiedot

Tallennettuna:
Bibliografiset tiedot
Julkaisussa:PLoS One
Päätekijät: Sutanto, Erika N., Scaffidi, Amelia, Garratt, Luke W., Looi, Kevin, Foo, Clara J., Tessari, Michela A., Janssen, Richard A., Fischer, David F., Stick, Stephen M., Kicic, Anthony
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: Public Library of Science 2018
Aiheet:
Research Article
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC5779693/
https://ncbi.nlm.nih.gov/pubmed/29360847
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0191618
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