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Inherited thrombotic thrombocytopenic purpura mimicking immune thrombocytopenic purpura during pregnancy: a case report

BACKGROUND: Thrombotic thrombocytopenic purpura is a very rare hereditary blood deficiency disorder of ADAMTS13 (von Willebrand factor-cleaving protease) and a life-threatening thrombotic microangiopathy characterized by thrombocytopenia and microangiopathic hemolytic anemia. The deficiency in ADAMT...

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Bibliografische gegevens
Gepubliceerd in:J Med Case Rep
Hoofdauteurs: Romão de Souza, Valter, Beatriz Cavalcante de Oliveira, Ana, Maria Vanderlei, Ana, Queiroz da Mota Silveira Aroucha, Amanda, Pontes Duarte, Bruna, Nunes Machado, Aureli, Netto Chaer, Lívia, Wanderley de Barros Correia, Cláudia, da Conceição de Barros Correia, Maria, Freire Hazin Costa, Manuela
Formaat: Artigo
Taal:Inglês
Gepubliceerd in: BioMed Central 2018
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Online toegang:https://ncbi.nlm.nih.gov/pmc/articles/PMC5778757/
https://ncbi.nlm.nih.gov/pubmed/29357939
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13256-017-1545-3
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