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Inherited thrombotic thrombocytopenic purpura mimicking immune thrombocytopenic purpura during pregnancy: a case report

BACKGROUND: Thrombotic thrombocytopenic purpura is a very rare hereditary blood deficiency disorder of ADAMTS13 (von Willebrand factor-cleaving protease) and a life-threatening thrombotic microangiopathy characterized by thrombocytopenia and microangiopathic hemolytic anemia. The deficiency in ADAMT...

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Détails bibliographiques
Publié dans:J Med Case Rep
Auteurs principaux: Romão de Souza, Valter, Beatriz Cavalcante de Oliveira, Ana, Maria Vanderlei, Ana, Queiroz da Mota Silveira Aroucha, Amanda, Pontes Duarte, Bruna, Nunes Machado, Aureli, Netto Chaer, Lívia, Wanderley de Barros Correia, Cláudia, da Conceição de Barros Correia, Maria, Freire Hazin Costa, Manuela
Format: Artigo
Langue:Inglês
Publié: BioMed Central 2018
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC5778757/
https://ncbi.nlm.nih.gov/pubmed/29357939
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13256-017-1545-3
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